[Incontinentia pigmenti: a rare cause of retinal vasculitis in children]

Incontinentia pigmenti is a genetic disease with cutaneous, dental, neurologic and ophthalmologic manifestations. Ocular changes are very varied. Retinal vasculitis is uncommon, but can be observed in this disease. To report a case of a patient with retinal vasculitis associated to Incontinentia pigmenti. A seven year old girl was followed for cutaneous lesions with the diagnosis of incontinentia pigmenti confirmed by a skin biopsy. She had delayed eruption of her teeth some of which were conical. She had no neurologic nor developmental abnormalities. Ophthalmological examination and fluorescein angiography was performed and showed retinal neovascularization in the left eye, secondary to retinal ischemia and retinal sequelae vasculitis without inflammation or complications in the right eye. Laser photocoagulation was indicated to the left and a strict surveillance to the right eye. After one month of the beginning of treatment, we noticed an involution of the retinal neovascularisation. Early diagnosis and management of retinal changes in incontinentia pigmenti is essential because they may be serious leading to blindness

[Ocular findings in megaloblastic anemia associated with diabetes. A case report]

Ocular involvements of Biermer's anaemia are rarely reported in literature. We present a case of Biermer's anaemia associated with diabetes. Ocular examination showed important conjinctival paleness, diffuse retinal ischemia, Roth's tasks, macular oedema and ischemic optic neuropathy. The patient was treated with vitamin B12 intramusculary. A month later, on examination, we noted a regression of optic neuropathy, the aggravation of ischemic retinopathy and persistence of macular oedema. The patient was treated with laser photocoagubation. The majority of ocular manifestations are reversible if treatment is undertaken early. The combination of diabetes with Biermer's anemia deteriorates the ischemic retinopathy and aggavates its prognosis

Syndrome de Lofgren revele par une tumeur palpebrale

The Lofgren syndrom is a particular variety of sarcoidose. The ocular attack is dominated in this syndrom by anterior uveitis. More rarely the eyelids and the orbitary structures ore attached. Purpose In this work, we report a lofgren syndrom case revealed by eyelid tumor. Observation It is about 42 year-oid patient who consults for a right inferior eye-lid tumefaction developped for 2 months. The diagnosis of Lofgren syndrome was evoqued because of the association of fever, arthritis, erythema nodosum, tuberculin anergia, hypercalcinuria and mediastinal adenopathy at thoracic scan-tomography. The diagnosis was then confirmed by biopsy of palpebral tumor which showed multiple epithe-lioid and gigantocellulor granuloma without caseous necrosis. Conclusion The Lofgren syndrome is a multivisceral chronic affection. The eye and its annexes constitute frequent cibles of this affection for which they react by a diverse and rich symptomalogy and which can be presented by eye-lid tumors with orbital extension